Back issues No.4 - 2007  
  Original Study
  Juvenile Pityriasis Rubra Pilaris in Chang Gung Memorial Hospital, Taipei and Linkou: A Retrospective Study in the Past Ten Years
Wan-Lung Lin , Wen-Chi Lin , I-Hsin Shih , Li-Cheng Yang , Hong-Shang Hong
Dermatol Sinica 25 : 248-255,2007

Pityriasis rubra pilaris (PRP) is an uncommon dermatosis in childhood. Only a few long-term studies to evaluate the course and prognosis of PRP in children have been done. In this study, we retrospectively reviewed the clinical manifestation, family history, course of the disease and response to treatment in 18 patients with PRP ages 18 years old or younger. These patients were seen at Chang Gung Memorial Hospital, Taipei and Linkou, between 1997 and 2006. Of the 18 patients, 11 were male and 7 ..................More
  Case Report
  Phacomatosis Pigmentokeratotica : A 4-month-old Infant with Rare Melanocytic–Epidermal Twin Nevus Syndrome-Case Report
Ching-Ying Wu , Wen-Yu Chang , Chieh-Shan Wu , Gwo-Shing Chen
Dermatol Sinica 25: 261-264, 2007

Abstract Phacomatosis pigmentokeratotica is a rare syndrome defined by the association of an organoid nevus occasionally with sebaceous differentiation, a speckled lentiginous nevus, and other extracutaneous anomalies. Such a combination of nevus sebaceous with melanocytic lesions may be explained by the concept of twin spotting. We describe a 4-month-old boy with a speckled lentiginous nevus arising from linear sebaceous nevus, intractable seizure, visual impairment, and hearing loss ..................More
  Traumatic asphyxia-report of two cases
Ching-Ying Wu , Gwo-Shing Chen , Hsinglin Lin
Dermatol Sinica 25: 261-264, 2007

Traumatic asphyxia is a rare clinical syndrome characterized by the triad of cervicofacial cyanosis and edema, bilateral subconjunctival hemorrhage, and cutaneous petechial hemorrhages of the face, neck and upper chest. We reported two cases of traumatic asphyxia following traffic accident that recovered without cutaneous or systemic sequelae. We also discuss the pathophysiology of this rare traumatic asphyxia. ..................More
  Mutation Analysis of TSC Gene in Tuberous Sclerosis Complex Patient-Case Report
Chiu-Yen Ho , Kuo-Chia Yang , Ming Chen , Shun-Ping Chang
Dermatol Sinica 25: 265-273, 2007

Tuberous sclerosis complex (TSC) is an autosomal dominant disorder characterized by hamartomas in many organs. Two thirds of cases are sporadic and are thought to represent new mutations. TSC is caused by mutations affecting either of the presumed tumor-suppressor genes, TSC1 and TSC2. Both appear to function as tumor suppressors, because somatic loss or intragenic mutation of the corresponding wild-type allele is seen in the associated hamartomas. We found a 47 year-old female patient suffered ..................More
  Proximal-Type Epithelioid Sarcoma-A Case Report and Review of the Literature
Hung-Yi Huang , Po-Han Wang , Wan-Ting Chiu , Yih-Yiing Wu , Shu-Ling Hu
Dermatol Sinica 25: 274-278, 2007

Proximal-type epithelioid sarcoma is a rare, malignant soft-tissue tumor occurring in the proximal body sites of young to middle-aged adults and microscopically shows sheets of large polygonal cells with vesicular nuclei, prominent nucleoli and frequent rhabdoid features. Herein, we report a 27-year-old woman with proximal-type epithelioid sarcoma over the pubic area. The patient underwent wide excision, left inguinal lymph node dissection and split-thickness skin graft after biopsy proof. Patho ..................More
  Multiple brownish nodules with blisters on the trunk and extremities
Pei-Ying Huang , Chia-Yu Chu
Dermatol Sinica 25: 285-286, 2007

CASE REPORT A 79-year-old gentleman presented with a 1-year history of many pruritic nodules on the trunk and extremities. Some blisters developed for several weeks before he visited our clinic. On physical examination, there were about 60 discrete, hyperkeratotic, brownish nodules on the trunk and four limbs (Fig. 1). Besides, there were several tense blisters right on some of the prurigo lesions and the normal skin (Fig. 2). No oral erosion or blister was found. Routine investigations includi ..................More
  Systemic Intravenous Corticosteroid Treatment of Adult Varicella Pneumonia
Chen-Hsi Hung , Tsu-Man Chiu
Dermatol Sinica 25: 287-288, 2007

CASE REPORT This 35-year-old man was in good health until 6 days prior to admission, when he experienced malaise, high-grade fever, and symptoms of upper respiratory infection. He developed skin rashes 6 days before admission after contacted with his own child with chickenpox. On arrival, a chest x-ray showed fluffy opacities over both lungs(Fig. 1). He was admitted to our dermatological ward under the impression of varicella pneumonia. After admission, he received acyclovir and Ampicillin/Su ..................More
  Resident Forum
  Novel Compound Heterozygous TGM1 Mutations in Lamellar Ichthyosis in Taiwan
Hsiu-Mien Chang , Cheng-Hui Lin , Sheau-Chiou Chao , Shao-Ping Chang
Dermatol Sinica 25: 279-281, 2007

A full-term female newborn was born encased in a yellow, tight, shiny collodion membrane with mild ectropion (Fig. 1). Her hair, teeth and nails appeared normal. She had no other congenital anomalies except the bilateral pre-auricular pits. Her parents are not consanguineous and no other family members had similar symptoms before. Since birth, she was placed in an incubator and bathed with warm normal saline. Vital signs and electrolytes were closely monitored to present from excessive transepid ..................More
  Eccrine Angiomatous Hamartoma with Features of Verrucous Hemangioma
Ching-Wen Huang , Ya-Ju Hsieh , Yu-Hung Wu , Yang-Chin Lin , Kuo-Ming Chuang
Dermatol Sinica 25: 282-284, 2007

A 43-year-old man presented with a solitary asymptomatic lump on his left lower leg present since early childhood. The lesion had enlarged slowly and become verrucous. There was no evidence of sweating in the lesion evoked by physical work or emotional stress. The patient was otherwise healthy. Physical examination disclosed a raised, 3 × 2-cm, purple-to-black hyperkeratotic plaque on the left shin (Fig. 1). Histopathologic examination of tissue from an excisional biopsy showed a hyperkeratotic ..................More
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