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Pachyonychia Congenita Type 2—A Case Report—
Fu-Sen Hsieh, J. Yu-Yun Lee, Sheau-Chiou Chao
Dermatol Sinica 19: 204-209, 2001

Pachyonychia congenita type 2 (PC-2), also known as Jackson-Lawler type PC, is a rare autosomal dominant disorder characterized by hypertrophic nail dystrophy associated with focal palmoplantar keratoderma and multiple pilosebaceous cysts. Only one case of PC-1 has been previously reported in Taiwan. In this report, we describe a typical case of PC-2, the first such case to be documented in Taiwan. The keratoderma was treated with etretinate, which was quite effective in reducing the hyperkeratotic lesions on the patient's palms and soles.

   
   
 
 
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