Back issues No.3 - 2001 / Case Report  

Full Text PDF


Pachyonychia Congenita Type 2—A Case Report—
Fu-Sen Hsieh, J. Yu-Yun Lee, Sheau-Chiou Chao
Dermatol Sinica 19: 204-209, 2001

Pachyonychia congenita type 2 (PC-2), also known as Jackson-Lawler type PC, is a rare autosomal dominant disorder characterized by hypertrophic nail dystrophy associated with focal palmoplantar keratoderma and multiple pilosebaceous cysts. Only one case of PC-1 has been previously reported in Taiwan. In this report, we describe a typical case of PC-2, the first such case to be documented in Taiwan. The keratoderma was treated with etretinate, which was quite effective in reducing the hyperkeratotic lesions on the patient's palms and soles.

You are visitors    
Copyright © 2008 THE Taiwanese Dermatological Association. All Rights Reserved. Email: Tel:886-2-2518-5126~7 Fax:886-2-2518-5128